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KMID : 1037820170060020046
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Journal of Pain and Autonomic Disorders
2017 Volume.6 No. 2 p.46 ~ p.50
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A Case of Autoimmune Autonomic Ganglionopathy Responding to Immunotherapy
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Na Seung-Hee
Lee Eek-Sung
Lee Tae-Kyeong
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Abstract
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Autoimmune autonomic ganglionopathy (AAG) is a rare disorder involving both cholinergic and noradrenergic autonomic pathways with progressive but monophasic disease course. Patients with AAG often have an antecedent event such as viral infection and show diverse autonomic dysfunction. Anti-ganglionic acetylcholine receptor antibody can be detected in about half of them. Based on pathophysiology, the response to immunotherapy is usually good. We experienced a patient with autoimmune autonomic neuropathy after a febrile illness responding to plasmapheresis following intravenous immunoglobulin.
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KEYWORD
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Autonomic nervous system, Ganglion, Autoimmune disease, Peripheral neuropathies, Immunotherapy
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